颅内软骨肉瘤罕见,本文报告了4例颅内软骨肉瘤并经手术切除和病理证实。男2例,女2例,平均年令35岁。4例都在颅底,其中3例在硬脑膜外,位于前颅窝底1例,蝶骨嵴1例,后颅窝1例;另1例在硬脑膜下位于蝶骨嵴。颅内软骨肉瘤的临床症状和体征不易与颅内相同部位的其他类型肿瘤相鉴别,主要靠组织学图象的表现特点区别。对本病的治疗,主要采取手术切除加放射等综合治疗措施,部分病人可以得到较为满意的效果。 Intracranial chondrosarcoma is rare, the paper reported four cases of intracranial chondrosarcoma and surgical resection and pathology confirmed. 2 males and 2 females, with an average age of 35 years. 4 cases were in the skull base, of which 3 cases in the dura, located in the anterior cranial fossa in 1 case, sphenoid ridge in 1 case, 1 case of posterior fossa; the other 1 case in the dural crest in the dural. Clinical symptoms and signs of intracranial chondrosarcoma difficult to differentiate from other types of tumors in the same part of the brain, mainly by the performance characteristics of histological differences. The treatment of this disease, the main surgical resection plus radiation and other comprehensive treatment measures, some patients can get more satisfactory results.