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典型的进行性神经性腓骨肌萎缩症(CMT)是一种常染色体显性遗传性周围神经病,伴有腱反射减低,和运动神经传导速度减慢.弓形足,远端肌肉无力及萎缩,周围神经肥大改变在本病中常见.以前曾报导关于CMT偶尔也发生视神经受累,实际上典型病人中这种伴随症出现的频度尚未完全确定,反相图形视觉诱发电位(PRVEP)是用以评定中枢视觉通路的功能的一种新技术.我们在25例CMT综合症的病人探讨了反相图形视觉诱发电位.
A typical progressive neuropathic Charcot-Marie-Tooth Syndrome (CMT) is an autosomal dominant hereditary peripheral neuropathy with reduced tendon reflexes and slowed motor nerve conduction velocity. The arch foot, distal muscle weakness and atrophy, Neuromuscular changes are common in this disease.It has previously been reported that the occurrence of optic neuropathy occasionally occurs in CMT, and in fact the frequency of such complications in a typical patient has not yet been fully established and the inverse visual pattern visual evoked potential (PRVEP) is used to assess A new technique for the function of central visual pathways.We investigated the reversal pattern visual evoked potential in 25 patients with CMT syndrome.