平滑肌肉瘤是一种通常发生于女性生殖道和胃肠道的恶性肿瘤,极少数发生于腹膜后腔和腹腔。平滑肌肉瘤也发生于软组织,占所有恶性软组织肿瘤的5%～10%,占新确诊的骨与软组织肉瘤的14%,相比之下,原发性骨平滑肌肉瘤罕见。Berlin等估计骨平滑肌肉瘤在瑞典每年的发病率是百万分之0.09。我国尚未见有关发病率的确切统计。Carmody等在1944年报道了1例发生于下颌骨的平滑肌肉瘤。Evans等在1965年报道了首例发生 Leiomyosarcoma is a malignant tumor usually occurring in the female reproductive and gastrointestinal tract, very rare in the retroperitoneal and abdominal cavity. Leiomyosarcoma also occurs in soft tissue, accounting for 5% to 10% of all malignant soft tissue tumors, accounting for 14% of newly diagnosed bone and soft tissue sarcomas, compared with rare cases of primary osteosarcoma. Berlin et al estimated that the annual incidence of leiomyosarcoma in Sweden is 0.09 parts per million. My country has not yet seen the exact statistics on the incidence. Carmody et al reported in 1944 1 case of mandibular leiomyosarcoma. Evans et al. Reported the first occurrence in 1965