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Prune-Belly综合征也称Triad综合征、Eagle-Barrett综合征、腹肌缺陷综合征、杏梅腹综合征及三联综合征(以下称PBS)。1895年Parker首先描述三联表现:腹肌缺陷、两侧隐睾、泌尿系多发畸形(巨膀胱及输尿管、肾发育不全等)。1901年Osler使用“Prune-Belly”综合的名称。国外报道300多例,日本报道82例。南医二附院收治一例,有局限性腹肌缺陷、两侧隐睾、右侧多囊肾、左侧重肾双输尿管。国内文献尚无其他报道及论述。本文就该病的病因、临床表现及处理作一综述。
Prune-Belly syndrome is also known as Triad syndrome, Eagle-Barrett syndrome, abdominal muscle defect syndrome, apricot syndrome and triad syndrome (hereinafter referred to as PBS). In 1895 Parker first described triple performance: abdominal defects, cryptorchidism on both sides, multiple urinary malformations (giant bladder and ureter, renal hypoplasia, etc.). In 1901 Osler used the name “Prune-Belly”. More than 300 foreign reports, 82 cases reported in Japan. Second Affiliated Hospital of Chinese medicine admitted to a case, there are limitations of abdominal muscle defects, both sides of cryptorchidism, right polycystic kidney, left kidney double ureter. Domestic literature no other reports and discussion. This article reviews the etiology, clinical manifestations and management of the disease.