本文报告9例经临床诊断和其中8例通过角膜镜面反射内皮显微镜检查证实的虹膜痣综合征病例。讨论了虹膜痣综合征的临床病理特点、病因与发病机理。证实虹膜痣综合征象虹膜角膜内皮(ICE)综合征的其他临床变异一样,具有相同的角膜内皮缺陷。而且虹膜痣综合征与Chandler 氏综合征有着临床上的联系。 This article reports 9 cases of clinically diagnosed cases and 8 cases of iris nevus syndrome confirmed by corneal specular reflection endoscopy. The clinicopathological features, etiology and pathogenesis of iris nevus syndrome were discussed. It has been shown that iris nevus syndrome, like other clinical variants of iris corneal endothelial (ICE) syndrome, has the same corneal endothelial defects. And Iris syndrome and Chandler’s syndrome is clinically linked.