男性假两性畸型—女性化综合症(Codberg—Maxuell 综合症)为临床上较罕见的先天性疾病,近年来,国内虽已有报导,但属家族性病例报导极少。我院82年2月收治一例家族性姊妹3人中2人属此畸型,并均做了染色体检查,其中一例经手术后组织切片证明,兹报告如下。例1:患者社会性别:女,22岁,未婚,住院号63217。因双侧腹股沟部肿物,来我院外科就诊。既往史:十岁时曾在本市某医院行右斜疝修补术,一年后复发。体检发现双侧腹股沟区分别可触及同等大小约6.5×5×3.5cm 的椭园形实质性肿物、左侧可还纳,而 Male pseudohermaphroditism - feminization syndrome (Codberg-Maxuell syndrome) is a rare clinical congenital disease, although there have been reports in recent years, but very few cases of familial reports. In our hospital in February 82 admitted to a case of familial sisters 3 of 2 people are abnormal, and have done a chromosomal examination, of which one case after the operation of tissue sections to prove, hereby report as follows. Example 1: Patient Gender: Female, 22 years old, single, hospital number 63217. Due to bilateral inguinal masses, to our hospital surgical treatment. Past history: At the age of ten had a right oblique hernia repair at a hospital in the city, a year later recurrence. Physical examination found that both sides of the inguinal region can reach the same size of about 6.5 × 5 × 3.5cm oval-shaped substantive tumor, the left can be satisfied, and