腹膜后淋巴管瘤临床少见，加之腹膜后部位深、间隙大，临床又无特征性表现，确诊困难。当肿块增大到一定程度对周围组织或脏器产生占位压迫症状而就诊，往往诊断为腹膜后其它肿瘤行手术切除，经病理检查才得以确诊。我科20年来共收治腹膜后肿瘤55例，经手术切除病理确诊为腹膜后淋巴管瘤9例。术前无一例明确诊断为腹膜后淋巴管瘤。 Retroperitoneal lymphangioma is rare in clinical practice, combined with deep retroperitoneal space, large gaps, and no clinically characteristic features, making diagnosis difficult. When the tumor enlarges to a certain degree, and the surrounding tissues or organs have the symptoms of occupational pressure compression, it is often diagnosed as other retroperitoneal tumors undergoing surgical resection. Only pathological examination can confirm the diagnosis. In our department for a total of 55 cases of retroperitoneal tumors in the past 20 years, 9 cases have been diagnosed with retroperitoneal lymphangioma after surgical resection. There was no clear diagnosis of retroperitoneal lymphangioma before surgery.