神经皮肤黑色素瘤综合征(NeurocutaneousMelanomatosis Syndrome)是先天性外胚叶发育异常所致的神经系统和皮肤同时出现的病变,临床罕见。作者目睹一例,表现为皮肤巨大兽皮样多毛和播种性黑色素斑、腰背部皮肤神经纤维瘤病及软脑膜和脑的黑色素瘤。目前国内文献尚未 Neurocutaneous melanoma syndrome (NeurocutaneousMelanomatosis Syndrome) is a congenital ectodermal dysfunction caused by the nervous system and skin lesions occur at the same time, the clinical rare. The authors witnessed an example of giant skin-like hirsutism and seeding melanoma, low back cutaneous neurofibromatosis and meningioma and brain melanoma. The current domestic literature has not yet