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肝豆状核变性是染色体隐性遗传性铜代谢障碍性疾病。病变可累及多脏器系统。然而肝豆状核变性对心脏的影响在国内极少报道。我院自1994年6月～1998年5月共收治肝豆状核变性患儿36例,均做心电图检查。其中有心电图改变者11例。现报道如下:1 一般资料11例患儿中男5例,女6例。年
Hepatolenticular degeneration is a chromosomal recessive genetic disorder of copper metabolism. Lesions can affect multiple organ systems. However, the impact of hepatolenticular degeneration on the heart is rarely reported in China. Our hospital from June 1994 to May 1998 were treated children with hepatolenticular degeneration in 36 cases, are doing electrocardiogram. There are 11 cases of ECG changes. Are reported as follows: 1 General Information 11 cases of children in 5 males and 6 females. year