球旁细胞瘤(Juxtaglomerular Cell Tu-mor)(亦称肾素瘤,或Robertson-Kihara 综合症)即可分泌大量肾素的肾小球旁器血管外皮细胞瘤。肿瘤形成原因未明,临床表现以高血浆肾素、继发性醛固酮增多,低血钾及严重高血压为特征。手术切除后,各种症状可完全消除。1967年Robertson 首先报道后,至今见于文献共16例。最初,本症仅在病理检查时得到证实;近年来,随着肾素尤其是分侧 Juxtaglomerular Cell Tu-mor (also known as renin, or Robertson-Kihara syndrome) secretes a large amount of renin-producing glomerular peritheamatous hemangiopericytoma. The cause of the tumor is unknown. The clinical manifestations are characterized by high plasma renin, secondary aldosterone, hypokalemia and severe hypertension. After surgical resection, various symptoms can be completely eliminated. Robertson first reported in 1967, so far found in the literature a total of 16 cases. Initially, the disease was confirmed only in pathological examination; in recent years, with renin, especially sub-side