目的:提高乳头状肾细胞癌的诊治水平。方法:8例均作影像学检查,IVU示患侧肾脏外形增大;CT示患侧肾脏有类圆形、界限清楚、中心有肿瘤坏死引起的低密度灶。8例患者均接受肾癌根治术,其中2例经腹腔途径,6例经11肋间切口。结果:随访4-60个月,除1例于术后13个月死于颅内转移外,其余均生存。结论:乳头状肾细胞癌是较罕见的肾细胞肿瘤,其形态学和遗传学与非乳头状肾细胞癌有明显不同;其确诊有赖于影像学检查、典型病理检查及分子遗传学特征分析;治疗仍以手术为主。 Objective: To improve the diagnosis and treatment of papillary renal cell carcinoma. Methods: All the 8 cases were examined by imaging examination. IVU showed increased shape of affected kidney. CT showed that the affected side of kidney had a round, well-defined border with low density lesions caused by tumor necrosis. All 8 patients underwent radical nephrectomy. Two of them underwent transperitoneal approach and six had underwent intercostal incision. Results: All cases were followed up for 4-60 months. Except one case died of intracranial metastasis at 13 months after operation, the rest survived. Conclusion: Papillary renal cell carcinoma (RCC) is a rare type of renal cell carcinoma with obvious difference in morphology and genetics and non-papillary renal cell carcinoma. Its diagnosis depends on imaging examination, typical pathological examination and molecular genetics analysis. The treatment is still based on surgery.