近十余年来由于对凝血因子Ⅷ及Ⅸ的深入研究加上对血浆凝血因子制品的生产不断改进,血友病患者的生存率已明显提高。在发达的国家中,血友病的治疗不仅限于出血期,而且涉及康复期的防治,有的国家普遍成立了血友病防治中心,广泛开展家庭防治。在这些方面我国还有很大差距。本文将目前血友病的临床研究概况略述于下。 In the recent ten years due to the in-depth study of coagulation factors Ⅷ and Ⅸ together with the continuous improvement of the production of plasma coagulation factors, the survival rate of hemophilia patients has been significantly improved. In developed countries, the treatment of hemophilia is not limited to the bleeding period, but also involves the prevention and treatment of convalescence. In some countries, a hemophilia prevention and control center has been set up and family prevention and control has been widely carried out. There is still a long way to go in these areas. In this paper, the current overview of clinical studies of hemophilia is outlined below.