婴儿肌纤维瘤病(先天性、全身性或多发性纤维瘤病、多发性间充质错构瘤、多发性血管平滑肌瘤)发生于新生儿期,约90％发生于1岁以内。内脏的肿瘤预后较差,但结局根据内脏病变的部位及范围而不同,通常由于侵犯心脏或胃肠道无法切除而死亡。病变可为单发或多发。婴儿多发性病变常侵犯骨骼、肺、心脏和肠道,胸腔内受累表现为间质性纤维 Infantile myofibromatosis (congenital, general or multiple fibromatosis, multiple mesenchymal hamartomas, multiple angiomyolipomas) occurs during the neonatal period and approximately 90% occurs within 1 year of age. The visceral tumor has a poor prognosis, but the outcome varies according to the site and extent of the visceral lesion, and usually dies as a result of inability to excise the heart or gastrointestinal tract. Lesions can be single or multiple. Infantile multiple lesions often violated the bones, lungs, heart and intestine, chest involvement showed interstitial fibers