着色性干皮病是一种罕见的皮肤病,自1870年Raposi报告首例以来,文献上陆续有所报道。该病在人群患病率达1/65,000～1/100,000,原发于皮肤及粘膜,但有眼部损害者约占80％,故患者多先就诊于眼科,我们于1984年遇见一例,报告如下: 病例报告患者,男,27岁,汉族。自述于5岁时,在一次“发热”后,全身出现红斑、痒。几天后,即脱落皮屑。随后,面部皮肤 Scleroderma is a rare dermatosis that has been reported in the literature since the first Raposi report in 1870. The disease in the population prevalence rate of 1 / 65,000 ~ 1 / 100,000, primary in the skin and mucous membranes, but there are about 80% of eye damage, so many patients first visited ophthalmology, we met in 1984, a report As follows: Case report Patient, male, 27 years old, Han nationality. Readme at 5 years old, after a “fever”, the whole body erythema, itching. A few days later, shedding dander. Then, facial skin