Sturge-Weber综合征,又称脑面血管瘤病,脑-三叉神经血管瘤病,皮肤-软脑膜血管瘤等,为一少见先天性疾病,国内报告不多,本文报告5例如下:1 临床资料例1,男,3岁。生后发现面部有一血管痣,逐渐长大,二年来反复发作性抽搐,近10个月,右侧上、下肢活动逐渐受限。体检智力差,左额部血管瘤10cm×6cm,上界入发际内4cm,右侧肌张力偏高,右上、下肢肌力Ⅲ级,右侧肌肉略萎缩,右侧巴彬斯基征阳性。CT表现:双额叶、左颞叶及顶叶皮质下均可见脑回状钙化斑,左侧裂池及纵池扩大,右额叶、顶叶脑沟明显加深加宽, Sturge-Weber syndrome, also known as cerebral hemangiomatosis, brain - trigeminal hemangiomatosis, skin - leptomeningeal hemangioma, is a rare congenital disease, the domestic report is not much, this report 5 cases are as follows: 1 clinical Example 1, male, 3 years old. After birth, a vasculitus was found on the face and gradually grew up. In the past two years, repeated episodes of seizures were reported. In the past 10 months, the upper and lower extremities gradually became limited in activities. Poor physical examination, left forehead hemangioma 10cm × 6cm, the upper bound within the hairline 4cm, the right side of the high muscle tension, upper right and lower extremity muscle strength Ⅲ, the right muscle slightly atrophy, right Babinski sign positive . CT manifestations: double frontal lobe, left temporal lobe and parietal cortex can be seen under the brain calcification plaque, the left fissure and longitudinal pool to expand the right frontal lobe, parietal lobe of the brain significantly deepened and widened,