先天性二叶主动脉瓣国外较常见,国内报道尚少。伴有三、四相束支阻滞的更罕见。现将我院见到的1例报道如下。一、临床资料患者,女性,56岁。曾发现心脏杂音14余年,3年来加重,近1个月感活动后头晕、胸闷及心前区痛。近3日间歇性晕厥、抽搐,于1986年10月住院。住院后查体S_1及A_2减弱,于胸骨右缘第二肋间可闻Ⅲ～Ⅳ级收缩期杂音,向颈部传导,胸骨左缘第三肋间闻 Congenital two-lobe aortic valve more common abroad, there are still few domestic reports. Accompanied by three or four phase bundle block more rare. Now I see the hospital reported the following 1 case. First, the clinical data Patients, women, 56 years old. Had found heart murmur more than 14 years, 3 years to aggravate, nearly 1 month after the activity of feeling dizzy, chest tightness and precordial pain. Nearly 3 days intermittent fainting, convulsions, hospitalized in October 1986. S_1 and A_2 of the examination after hospitalization weakened in the second right intercostal stenosis can be heard Ⅲ ~ Ⅳ systolic murmur, conduction to the neck, left sternal third intercostal smell