近年来,随着免疫理论和技术的发展,免疫缺陷病逐步引起了人们的注意。最近报道日本儿童原发性免疫缺陷病的发病率与小儿白血病近似。为了总结经验,兹将我科收治的一例原发性免疫缺陷病的临床及病理解剖资料报告如下。 In recent years, along with the development of immune theory and technology, immunodeficiency disease has gradually attracted people’s attention. The incidence of primary immunodeficiency in Japan has recently been reported to be similar to childhood leukemia. In order to summarize the experience, we will treat one case of primary immunodeficiency disease clinical and pathological anatomy data are reported as follows.