1974～1976三年中,通过病理解剖共发现6例先天性胸腺发育不全症。我们着重对胸腺、淋巴组织和付甲状腺进行了病理形态观察,现将结果报告如下。一般资料 6例中男2例,女4例。年令最小3月,最大17月。5例胸片中3例不见胸腺阴影。6例血常规提示有不同程度的贫血、周围血淋巴细胞绝对值均不低于1200/mm~3。5例查结核菌素试验均阴性,1例DNCB试验阴性。除例1有过抽搐外,其余5例未询问出抽搐史。住院日数最短8天,最长38天;合 During the three years from 1974 to 1976, a total of 6 cases of congenital thymus hypoplasia were found by pathological dissection. We focus on the thymus, lymphoid tissue and pay thyroid pathological observation, the results reported below. General information in 6 cases, 2 males and 4 females. Year minimum March, maximum 17 months. In 5 cases of chest radiographs, no thymus shadow was observed in 3 cases. 6 cases of blood showed different degrees of anemia, the absolute value of peripheral blood lymphocytes were not lower than 1200 / mm ~ 3.5 cases of tuberculin test negative, 1 case of DNCB test negative. In addition to cases of convulsions in 1, the remaining 5 cases did not ask the history of convulsions. Hospitalization days the shortest 8 days, up to 38 days;