弥漫性肺淋巴管瘤病(DPL)是一种具有潜在侵袭性的肺进行性疾病,好发于儿童和青年人,男女发病均等。该病以胸膜、胸膜下小叶间隔内和沿支气管血管淋巴途径出现大量复杂的、互相吻合的淋巴管为特征。作者介绍了8例经病理证实的DPL的CT表现,年龄3～35岁(平均15岁),男女各4例。所有病例均行胸部常规CT扫描(10mm准直),其中5例加作高分辨率CT扫描(1～1.5mm准直,高空间分辨力重建算法)。6例行静脉增强扫描。CT设备采用Picker 1200SX和GE9800扫描机。8例均经开胸活检病理证实为DPL。其诊断标准为:在胸膜、纵隔、肺门周围、小叶间隔和支气管血管及淋巴管周围出现大量复杂的淋巴管吻合,也可能会伴有平滑肌细 Diffuse pulmonary lymphangioma (DPL) is a potentially aggressive lung progressive disease that occurs in children and young adults, with equal incidence among men and women. The disease is characterised by the presence of a large number of complex, matched lymphatic vessels within the pleura, subpleural space, and along the bronchial vascular lymphatic pathway. The authors presented CT findings of 8 cases of pathologically confirmed DPL, aged 3 to 35 years (mean 15 years old), 4 males and 4 females. All patients underwent conventional chest CT scan (10mm collimation), of which 5 were included as high-resolution CT scans (1 to 1.5mm collimation, high spatial resolution reconstruction algorithm). 6 routine intravenous enhanced scan. CT equipment uses Picker 1200SX and GE9800 scanners. All 8 cases were pathologically confirmed by open thoracic biopsy as DPL. The diagnostic criteria are: a large number of complicated lymphatic anastomosis around the pleura, mediastinum, around the hilum, interlobular septum, and bronchial and lymphatic vessels, may also be associated with smooth muscle