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肠病性肢端皮炎是主要发生于儿童的一种罕见的家族性疾病。国内外有关本病的报导甚少,1942年Danbolt和Closs首先描述本病,并提出诊断本病的三大主要症状:①特殊的皮疹(好发于身体的腔口周围和末端);②腹泻,③脱发。此外病人还可能有舌炎、口炎、畏光、结膜炎、甲沟炎、指甲萎缩,精神紊乱等,并常伴发皮肤和粘膜的细菌或霉菌感染。为提高对本病的认识,现将我院遇到的一例报导如下。患儿女性,年龄1岁10个月,因身体腔口周围肢端部位的皮肤反复起水疱、破溃、结痂,伴双下肢浮肿二十余天而入院。患儿为足月顺产第二胎,以母乳为主。其兄、父母均无
Enteropathic acral dermatitis is a rare familial disease that occurs mainly in children. There are few reports about this disease at home and abroad. In 1942, Danbolt and Closs firstly described the disease and proposed three main symptoms of the diagnosis of the disease: (1) special rashes (appearing around and at the mouth of the body); (2) diarrhea , ③ hair loss. In addition the patient may also have glossitis, stomatitis, photophobia, conjunctivitis, paronychia, nail atrophy, mental disorders, and often accompanied by skin and mucous membranes of bacteria or fungal infections. In order to improve our understanding of this disease, we report the following one case encountered in our hospital. Children with children, aged 1 year and 10 months, due to repeated body acuity of the skin around the extremities blisters, ulceration, crusting, accompanied by lower extremity edema more than 20 days and admission. Children with full-term second trimester of birth to breast-based. His brother, no parents