原发于骨内的神经纤维肉瘤极少见 ,现我们遇一病例经手术病理证实报告如下。1　临床资料患者男性 ,36岁。无明显诱因出现左臀部反复疼痛 8个月 ,在行走或下蹲时疼痛明显 ,近两个月出现行走时跛行 ,疼痛加剧 ,伴左髋部肿胀明显。检查 :患者左下肢轻度跛行步态 ,左侧臀中肌压痛明 Primary intramedullary nerve fiber sarcoma rare, now we encounter a case confirmed by surgical pathology as follows. 1 clinical data of patients male, 36 years old. There was no obvious incentive for repeated pain in the left buttock for 8 months. The pain was obvious when walking or squatting, and limp in walking in the past two months. The pain worsened and the left hip swelled obviously. Check: Patients with mild left leg limping gait, left gluteal muscle tenderness