功能性单心室是一组复杂的发绀型先天性心脏病,其心功能评估和治疗一直备受关注。近年来,在心功能评估方面,应用组织多普勒反映心室的收缩和舒张功能;通过速度向量成像技术反映局部心肌组织真实的运动方向和大小;通过磁共振技术更为准确地计算出功能性单心室的各项心功能指标。在治疗方面,镶嵌治疗是一种新的手术模式,另外对于行房坦手术后心力衰竭的功能性单心室患者,最近研制的人造右心室的轴流泵提供一种新的治疗方向。 Functional single ventricle is a complex set of cyanotic congenital heart disease, its cardiac function evaluation and treatment has been of great concern. In recent years, in cardiac function assessment, the application of tissue Doppler reflects the ventricular systolic and diastolic function; velocity vector imaging technology to reflect the real direction of the local myocardial movement and size; by magnetic resonance technology to more accurately calculate the function of a single Ventricular heart function indicators. Mosaic treatment is a new surgical modality for treatment, and a recently developed axial pump for artificial right ventricle provides a new therapeutic direction for functional single-ventricular patients who have heart failure after catarrhal surgery.