淋巴瘤样肉芽肿病(lymphomatoid granulomatosis,简称LyG)是侵犯全身多种脏器特别是肺组织的一种淋巴增生性疾病。本病由Liebow等于1972年首先描述,病理上以血管中心性和血管破坏性的肉芽肿病变为特征。本病国外报道,并非少见,在临床和X线上与Wegener肉芽肿(特别是局限型)、血管免疫母细胞性淋巴腺病(AILD)和肺那淋巴瘤等疾病有许多相似之处,故在肺部疾病的鉴别诊断中也是不可忽视的。 Lymphomatoid granulomatosis (LyG) is a lymphoproliferative disorder that affects various organs of the body, especially lung tissue. The disease was first described by Liebow et al. In 1972, characterized by pathological central and vascularized granulomatous lesions. The foreign reports of the disease is not uncommon, clinical and X-ray and Wegener granuloma (especially localized), angioimmunoblastic lymphadenopathy (AILD) and lung lymphoma and other diseases have many similarities, so In the differential diagnosis of lung disease can not be ignored.