患儿、女、G1P1足月顺产,脐带长度16cm,脐水平中线右侧2.0cm处可见纵向裂孔约40cm长,裂孔处膨出结肠和大部分小肠,肠管明显水肿,增厚,肠襻相互粘连,伴有胎粪色纤维素假膜,肠管呈暗红色,浆膜下有血肿。因家属放弃治疗,未给予相应的措施。讨论:先天性腹裂极罕见,伴脐带过短者更罕 Children, women, G1P1 term full-term, umbilical cord length 16cm, umbilical horizontal midline 2.0cm at the right side of longitudinal cracks can be seen about 40cm long, cracked bulging colon and most of the small intestine, bowel obvious edema, thickening, intestinal adhesions , With meconium-colored cellulose pseudomembranous, bowel dark red, serosal hematoma. Due to family members to give up treatment, did not give the appropriate measures. Discussion: Congenital abdominal cracking is extremely rare, with umbilical cord is more rare