极重度进行性耳硬化症(VFAO)指耳硬化症病人,在标准临床听力计不能测得气导和骨导阈值(空白听力表),而重度进行性耳硬化症(FAO),按House等介绍,其气导水平超过85dB,骨导在各语言听觉频率均不能够测得。报告3例极重度耳硬化症患者,全部施行活塞型镫骨手术,获得了不同程度的满意效果。术中所见病理为厚足板贴附着致密而含血管的粘骨膜,再加鼓岬骨质突出,导致窗龛变狭。CT扫描检查显示耳囊软骨内骨层有广泛脱矿质区。重度进行性感音神经性聋除FAO和 Critically ill patients with otosclerosis (VFAO) are referred to as otosclerosis patients who can not measure air conduction and bone conduction threshold (blank audiometry) in a standard clinical audiometer, while severe progressive otitis (FAO), according to House et al. Introduction, the air conduction level of more than 85dB, bone conduction in the language auditory frequency can not be measured. Reported in 3 cases of patients with severe otosclerosis, all the implementation of the piston type stapes surgery, obtained varying degrees of satisfactory results. The pathological findings of thick plate attached to a thick plate with vascular mucosa, plus prominence prominence bony prominence, resulting in narrow niche window. CT scan revealed a wide range of demineralization in the ear cartilage. Severe sensory hearing loss of neurological deaf and FAO