［病例］男，２９岁。主因乏力，右上腹胀痛，餐后加重 ２周，伴右肩肿区疼痛，发现浓茶样尿液１０天，于１９９９年４月２４日入院。行腹部Ｂ超检查示“肝硬化？”。追问病史，患者４岁起每遇日晒后面部、四肢等暴露部位出现疼痛性红斑，愈后有色素沉着，对透过玻璃的光线也能 [Case] ​​Male, 29 years old. The main cause of fatigue, right upper quadrant pain, increased postprandial 2 weeks, with pain in the right shoulder swollen area and found concentrated tea-like urine for 10 days, on April 24, 1999 admission. Abdominal ultrasound B line shows “cirrhosis?” Question history, the patient from the age of 4 each encounter sun after the face, limbs and other exposed parts of painful erythema, the more pigmentation, the light through the glass can