先天性主动脉畸形是导致主动脉夹层的罕见病因。我院收治1例先天性主动脉闭锁致继发性高血压合并降主动脉夹层的患者,报告如下。患者男,51岁,因发现血压增高34年,腹痛2天于2004年3月22日住入我院。患者17岁体检时发现血压升高,为170/110mm Hg(1mm Hg=0·133kPa),无自觉症状,未 Congenital aortic malformations are a rare cause of aortic dissection. A hospital admitted to our hospital with congenital aortic atresia secondary to hypertensive patients with aortic dissection, the report is as follows. Male, 51 years old, was found to have had an increase in blood pressure 34 years and had abdominal pain 2 days admitted to our hospital on March 22, 2004. Patients 17-year-old physical examination found elevated blood pressure, 170 / 110mm Hg (1mm Hg = 0 · 133kPa), no symptoms, not