特发性乳糜性心包积液(primary idiopathic chylopericardiunt)也称为原发性乳糜性心包积液,主要指无确切的病因时心包腔内积聚乳糜液。本病国内外临床报道较少且病因不清。本文报告2013年4月我院胸外科收治的1例特发性乳糜性心包积液,并结合文献对此疾病的临床表现、特征、诊断及治疗等进行复习讨论,以提高对此疾病的认识。1典型病例患者,女,23岁,主因“体检发现心包积液1 Primary idiopathic chylopericardiunt also known as primary peritoneal effusion, mainly refers to the absence of the exact cause of pericardial accumulation of chylothorax. The disease less clinical reports at home and abroad and the cause is unclear. This article reports a case of idiopathic chylous pericardial effusion admitted to our department of thoracic surgery in April 2013 and reviewed the clinical manifestations, characteristics, diagnosis and treatment of the disease in combination with the literature to improve understanding of the disease . A typical case of patients, female, 23 years old, mainly due to ”physical examination found pericardial effusion 1