近来认为多内分泌缺陷综合征包括两个特殊的病征。一个是在平均年龄12岁发病,原发性肾上腺皮质功能低下以及皮肤粘膜念珠菌病伴有甲旁低为其特征。也表现秃发,恶性贫血,营养吸收不良和慢性活动性肝炎。最近称这种病为多内分泌缺陷综合征Ⅰ型。其遗传类型尚不大清楚,但曾观察到某些家族中常染色体有缺陷。第二种病征在平均年龄30岁发病,原发性肾上腺皮质功能低下,合并自家免疫性甲状腺疾病,及胰岛素依赖型糖尿病。这种多腺 Recently, polyendocrine syndrome is thought to include two specific symptoms. One is characterized by an average age of 12 years of age, primary adrenal insufficiency, and mucocutaneous candidiasis with parathyroidism. Also shows alopecia, pernicious anemia, malabsorption and chronic active hepatitis. Recently said the disease is polyendocrine syndrome type Ⅰ. The genetic type is not yet clear, but some families have observed autosomal defects. The second symptom onset in the average age of 30 years, primary adrenal insufficiency, with autoimmune thyroid disease, and insulin-dependent diabetes mellitus. This polygamy