本文报告1例双侧中线旁丘脑梗塞综合征,表现暂时性昏迷,继而出现高度嗜睡状态、Korsakoff 遗忘综合征、皮质下痴呆、丘脑忽略,视觉立体空间障碍和垂直性注视麻痹,病变位工夫于中脑～丘脑结合处。作者进行了丘脑功能观察,提出脑诱发电位有助于临床观察,并结合文献对神经解剖与神经心理学机制进行复习和讨论。 This article reports one case of bilateral midline hypothalamic infarct syndrome, the performance of a temporary coma, followed by a high degree of drowsiness, Korsakoff amnestic syndrome, subcortical dementia, hypothalamic neglect, visual stereoscopic space disorders and vertical gaze paralysis, Midbrain ~ thalamus junction. The authors conducted a study of thalamic function, raised brain evoked potentials contribute to clinical observation, combined with the literature on neuroanatomy and neuropsychological mechanisms for review and discussion.