成人巨结肠类缘病也称赫什朋相关疾病 ,它不同于典型的先天性巨结肠 ,非常少见且易于漏诊。近年我们遇 1例 ,报告如下。1　病历简介　　女 ,37岁。间歇性腹胀、便秘 2 .5年 ,近 6个月病情加重 ,完全依靠灌肠排便。追问病史 ,儿童期似有间歇性便秘史。X线检查示降结肠扩张。查体 Hirschsprung’s disease is also known as Hirschborn disease, it is different from the typical Hirschsprung’s disease, is very rare and easy to miss. In recent years, we encountered a case, the report is as follows. 1 medical records Female, 37 years old. Intermittent abdominal distension, constipation 2.5 years, nearly 6 months exacerbations, relying solely on enema defecation. Asked history, childhood seems to have intermittent constipation history. X-ray examination showed decreased colon dilatation. Physical examination