诺西那生“诞生记”

来源 :科学画报 | 被引量 : 0次 | 上传用户：heirenmading

【摘要】

：

追溯疾病的发现过程rn脊髓性肌萎缩症的发现可追溯到19世纪90年代.1891年,奥地利神经疾病学家圭多·韦德尼格最先描述两位兄弟患儿.1893-1900年,德国神经疾病学家约翰·霍夫曼进一步描述7位患儿.他们注意到这些患儿在出生后几个月内就出现不同程度的肌无力,且疾病发生具有一定家族性.他们进一步研究发现,这些患儿脊髓前角部位的运动神经元出现退化,正是这一原因导致骨骼肌功能受损.为纪念两位科学家,Ⅰ型脊髓性肌萎縮症又被称为“霍夫曼-韦德尼格病”.

【作者】

：

郭晓强郭贝一

【机构】

：

河北体育学院;北京体育大学

【出处】

：

科学画报

【发表日期】

：

2022年1期

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