患者　女 ,13岁。于 2 0 0 3年 2月发现双面颊部出现红斑 ,日晒后加重 ,伴轻度瘙痒 ,症状渐加重 ,无诱因出现右上肢抽搐 ,伴口吐白沫 ,双眼向右上方凝视 ,牙关紧闭 ,小便失禁 ,可自行缓解 ,反复发作 10余次。体检 :嗜睡 ,心、肺、腹检查未见异常。双侧肢体肌力Ⅳ级 ,四肢腱反射 Female patient, 13 years old. In February 2003, erythema was observed on both cheeks. After the sun was aggravated, with slight itching, the symptoms gradually increased. There was no incentive to convuls the right upper extremity with foaming on the mouth and the eyes were staring right and above. Closed, urinary incontinence, relieve itself, recurrent episodes more than 10 times. Physical examination: lethargy, heart, lung, abdominal examination no abnormalities. Bilateral limb muscle Ⅳ grade, limb tendon reflex