本文报导５０例皮肤粘膜淋巴结综合征的Ｘ线表现，是以肺间质的病变为主，肺门及肺纹理的改变是最基本的Ｘ线表现，若患儿伴有皮肤粘膜损害和心脏改变，诊断不难确立，作者体会通过该综合征的再识认有利于Ｘ线诊断拓宽思路，密切结合临床资料，实验检查，心电图及Ｂ超，小儿胸片短期复查，动态观察，最终提高Ｘ线诊断正确率。 This article reports the X-ray findings of 50 cases of mucocutaneous lymph node syndrome, the main interstitial lung disease, hilar and lung changes in the most basic X-ray findings, if the children with skin and mucosal damage and cardiac changes , The diagnosis is not difficult to establish, the author realized through the re-recognition of the syndrome is conducive to X-ray diagnosis to broaden the thinking, combined with clinical data, laboratory tests, ECG and B-ultrasound, short-term review of pediatric chest, dynamic observation, and ultimately improve X-ray Diagnose the correct rate.