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β-珠蛋白生成障碍性贫血是一组起因于β珠蛋白基因表达缺陷,β珠蛋白生成减少而导致α/β珠蛋白链比率失衡的遗传性溶血性疾病。基于Bradai等应用羟基脲治疗7例重度珠蛋白生成障碍性贫血取得满意疗效,本研究应用羟基
β-globin aplastic anemia is a group of hereditary hemolytic diseases that result from the imbalance of α / β globin chain due to the defective expression of β-globin gene and the decrease of β-globin production. Based on Bradai and other applications of hydroxyurea treatment of 7 cases of severe hemoglobin aplastic anemia achieved satisfactory results, the study uses hydroxy