腺样囊性癌(adenoid cystic carcinoma,ACC)最常发生于头颈部的大小唾腺,少见于呼吸道、泪腺、乳腺、子宫、皮肤等处,食管原发性ACC临床上罕见~([1])。我们遇到1例食管原发性ACC,术前胃镜活检曾误诊为食管鳞状细胞癌,现结合文献探讨其组织起源及临床病理学特点。 Adenoid cystic carcinoma (ACC) occurs most frequently in the head and neck salivary glands, rarely in the respiratory tract, lacrimal gland, breast, uterus, skin and other places. ]). We encountered a case of primary esophageal ACC, preoperative gastroscopy biopsy has been misdiagnosed as esophageal squamous cell carcinoma, are combined with the literature to explore the origin of the organization and clinicopathological features.