遗传性舞蹈病国内报导的不多,本病为常染色体显性遗传,好发于中年(30～50岁),此病的主要病变区为大脑皮质、基底核,因病程较长,又呈慢性进行发展,故称慢性进行性舞蹈病。此病首先被Huntington氏发现又称为Huntington氏病,临床表现主要是舞蹈样不随意运动,早期有智能减退并呈进行性痴呆。近年来除对各地区发病 Hereditary chorea few domestic reports, the disease is autosomal dominant, occurs in middle age (30 to 50 years of age), the disease is the main lesion area of ​​the cerebral cortex, basal ganglia, due to longer duration, and Chronic progressive development, it is called chronic progressive chorea. The disease was first discovered by Huntington, also known as Huntington’s disease, the clinical manifestations are mainly dance-like involuntary movement, early decline and progressive dementia. In recent years, in addition to the incidence of various regions