目的　为重度先天性上睑下垂寻求更好的手术方法 ,以达到功能矫正和美学更佳的双重效果。方法　选择重度先天性上睑下垂 3 6眼行提上睑肌缩短术联合上横韧带固定术。结果　术后早期平视睑裂 6mm者 3 3眼 ( 91 7% ) ,上睑缘弧度及双重睑形成良好 ,双侧眼窝深度对称。术后仅部分病例早期有轻度闭合不全 ,1例一过性轻度结膜脱垂。结论　该术式在改善提睑功能和取得美学效果两方面对矫正重度上睑下垂都达到良好效果 Aims To seek better surgical methods for severe congenital blepharoptosis to achieve the dual effect of functional correction and aesthetics. Methods Severe congenital blepharoptosis 36 eyes with levator aponeurosis combined with supraspinatus ligament fixation. Results There were 33 eyes (91.7%) with palpation of palpebral fissure in the early stage after palpation of the palpebral fissure. The curvature of the upper eyelid and the formation of double eyelid were well, and the depth of both eyes was symmetrical. Only a few cases of early postoperative mild incomplete closure, 1 case of transient mild conjunctival prolapse. Conclusions This technique is effective in improving the eyelid function and obtaining aesthetics both in the correction of severe ptosis