本病系脑血管病中少见类型。主要发生在女婴及年轻成人中,其特征是颈动脉、脑底动脉终末部分闭塞、狭窄,并有包括动脉穿枝及软膜动脉等细血管交通网产生,晚期时还有其他血管交通网形成,包括颈外动脉眶枝与筛窦枝通过硬膜的软脑膜枝。现在世界各地均有报道,但本病病因不清,多数作者认为这是一型 The disease is a rare type of cerebrovascular disease. Mainly occurs in baby girls and young adults, which is characterized by carotid artery, the terminal part of the cerebral artery occlusion, stenosis, and including arterial perforation and soft membrane arteries and other fine vascular traffic network, there are other late vascular traffic Mesh formation, including the external carotid artery and ethmoid sinus branch through the dura mater of the meninges. Now all over the world are reported, but the etiology of this disease is unclear, most authors think this is a type