我们自1975年以来手术治疗8例先天性外耳道闭锁患者,遇到2例罕见面神经垂直端走向异常。现报告如下,并就面神经与有关中耳发育畸变的相互关系略加讨论。例1.男,9岁。双耳廓严重畸形合并外耳道闭锁,伴有Treacher-Collins综合征及左上肢桡骨小头畸形。手术发现相当于颞颌关节浅面,可见较粗大的面神经分支进入腮腺。骨体外耳道为一横行骨缝,凿开暴露鼓室,鼓室小而浅,镫骨、槌骨缺失,砧骨发育不良。面神经重直端缩短,横行前拐,在鼓室底前入颞颌关节浅面。例2.男,29岁。左先天性小耳合并外耳道闭 We have operated on 8 patients with congenital external auditory canal atresia since 1975, and we encountered 2 cases of abnormal vertical facial nerve anomalies. The report is presented below and a brief discussion of the interrelationship between facial nerve and related malformations of middle ear development. Example 1. Male, 9 years old. Severe malformations of both ears with external auditory canal atresia, with Treacher-Collins syndrome and left upper extremity radial head deformity. Surgical discovery is equivalent to the temporomandibular joint superficial, showing larger facial nerve branches into the parotid gland. External auditory canal is a transverse suture, open the tympanic exposed tympanum, tympanic small and shallow, stapes, mallet missing, incus dysplasia. Facial nerve weight shortened straight, ramp before the turn, at the tympanic floor into the temporomandibular joint shallow. Example 2. Male, 29 years old. Left congenital small ear merged with external auditory canal closed