干燥综合征(Sj?gren’s syndrome,SS)腺体外系统受累较常见,包括肺部病变。SS肺损害定义为出现呼吸道症状、肺功能异常或影像学异常等。患者表现各异,支气管炎和支气管扩张是常见的气道病变。SS合并间质性肺疾病是常见的肺部病变。另外,SS患者有患肺淋巴瘤的高风险,也可出现肺动脉高压、肺囊性病变、肺淀粉样变及胸膜受累等。基线评估SS患者肺部病变是必要的。目前关于SS合并肺损害的治疗尚缺乏大型、随机对照临床研究数据。进展性肺损害患者,糖皮质激素和(或)免疫抑制剂治疗是必要的。SS-肺动脉高压的治疗目前推荐靶向药物治疗为主。 Sjögren’s syndrome (SS) extragalactic system involvement is more common, including lung disease. SS lung damage is defined as respiratory symptoms, abnormal lung function, or imaging abnormalities. Patients perform differently and bronchitis and bronchiectasis are common airway diseases. SS with interstitial lung disease is a common lung disease. In addition, SS patients have a high risk of suffering from pulmonary lymphoma, pulmonary hypertension can also occur, cystic lung disease, pulmonary amyloidosis and pleural involvement. Baseline assessment of SS patients with pulmonary disease is necessary. Currently there is a lack of large, randomized, controlled clinical data on the treatment of SS complicated with lung damage. Patients with progressive lung damage, glucocorticoids and / or immunosuppressive agents are necessary. SS-Pulmonary Hypertension Treatment Targeted drug therapy is currently recommended.