马凡氏综合征(Marfans Syndrome),病因尚未十分明确,主要为骨骼系统,眼部及内脏病变。有人提出诊断本征须具备下列4项中的2项或2项以上。1、心血管病征:常有特殊的主动脉病变。2、骨骼系统病征:特别是蜘蛛状足样指。3、眼病征:主要是晶体异位。4、家族史。例1 叶××,女,19岁,工人,76年5月26日因视力不佳来门诊。病员从小视力不佳,家庭中父母视力均好,姊妹4人,2个妹 Marfan syndrome (Marfans Syndrome), the etiology is not yet clear, the main skeletal system, eye and visceral lesions. It has been proposed that the diagnostic eigenvector should have two or more of the following four items. 1, cardiovascular disease: often have special aortic lesions. 2, skeletal system symptoms: especially spider-like foot-like means. 3, eye symptoms: mainly ectopic. 4, family history. Example 1 leaves × ×, female, 19 years old, workers, May 26, 76 due to poor vision to the clinic. Patients with poor vision from early childhood, parents have good eyesight, sisters four people, two sisters