中心凹图案状色素上皮营养不良 (patterned pigment dys-trophy of the fovea)是一种少见的具有遗传性质的疾病。 Deut-man[1 ]报道一家族 4个成员有蝶形色素沉着于中心凹 ,此类病例已往文献未见报道。由于色素上皮受损脱失的色素 ,游离至中心凹周围 ,重新排列 ,形成各种各样的 A patterned pigment dys-trophy of the fovea is a rare, hereditary disease. Deut-man [1] reported that four members of a family have butterfly pigmentation in the fovea, such cases have not been reported in the literature. Due to pigment epithelial damage lost pigment, free to around the fovea, re-arranged to form a variety of