目的探讨不典型肺硬化性血管瘤(PSH)的CT特征。方法收集6例CT表现不典型、经病理证实的PSH患者影像学资料,分析其CT表现。结果 6例CT平扫表现如下:5例单发,其中3例表现为侧胸壁胸膜肿块、2例跨越斜裂胸膜生长,1例弥漫多发,贴近斜裂胸膜生长;4例形态不规则,2例呈类圆形或结节样;5例边缘见磨玻璃影;胸腔积液1例;囊变3例;粗点状钙化4例。5例接受CT增强扫描,动脉期3例轻度强化、1例中度强化、1例明显强化,静脉期3例强化程度稍增强、1例持续强化、1例CT值稍下降;均见贴近肿瘤边缘走行的血管影。结论不典型PSH CT多表现为不规则肿块,亦可呈多发结节状,可沿侧胸膜或跨越叶间胸膜生长,或伴胸腔积液。 Objective To investigate the CT features of atypical pulmonary sclerosing hemangioma (PSH). Methods Six cases with atypical CT findings and pathologically confirmed PSH were collected and their CT findings were analyzed. Results The CT findings of the 6 cases were as follows: 5 cases were solitary, of which 3 cases showed side pleural thoracic mass, 2 cases crossed obliquely cracked pleura, 1 diffusely plentiful and close to obliquely cracked pleura; 4 cases were irregular in shape, 2 Cases were round or nodular; 5 cases of edge see ground glass; pleural effusion in 1 case; 3 cases of cystic; coarse dotted calcification in 4 cases. Five patients underwent enhanced CT scan. Three patients in the arterial phase had mild enhancement, one in moderate enhancement and one in intensive enhancement. Three patients in the venous phase enhanced slightly, one continued to strengthen and one patient had a slight decrease in CT value. All were close Vascular shadow of tumor walking on the edge. Conclusions Atypical PSH CT often presents as an irregular mass. It may also show multiple nodules, pleural or lateral pleural growth, or pleural effusion.