比埃·洛宾综合征(PRS)的诊断标准是小颌、舌下垂和不全腭裂,偶尔病人可不具备其中某一特征。估计本病的发病率占出生人口的1∶2000到1∶50000。本资料回顾自1977～1987年10年间亚历克山大皇家儿童医院收治的伴有气道阻塞的PRS婴儿,共26例。其中男性15例,女性11例。出生体重范围在900～4 300g(平均3 000g)。8例有小颌和腭裂的家族史。25例软腭裂,其中13例合并硬腭裂。本病引起 The diagnostic criteria for Bourbon-Rabin syndrome (PRS) are small jaws, sagging, and incomplete cleft palate. Occasionally, a patient may not have one of these features. The incidence of this disease is estimated to account for 1: 2000 to 1: 50,000 of the birth population. This data reviews 26 cases of PRS infants with airway obstruction admitted to the Great Royal Children’s Hospital in Alexandria from 1977 to 1987. Including 15 males and 11 females. Birth weight range 900 ~ 4 300g (average 3 000g). Eight patients had a family history of small jaw and cleft palate. 25 cases of cleft palate, including 13 cases with cleft palate. The disease caused