Duodenal duplication cysts are rare congenital abnormalities which are more commonly diagnosed in infancy and childhood.However,in rare cases,these lesions can remain asymptomatic until adulthood.The combination of duplication cyst and pancreas divisum is extremely rare and both conditions have been linked with acute recurrent pancreatitis.We present the case of a 37 years-old patient who presented with repeated episodes of acute pancreatitis.By means of magnetic resonance imaging and endoscopic ultrasonography we discovered a duplication cyst whose cavity received drainage from the dorsal pancreas.After opening the cyst cavity to the duodenal lumen with a needle knife the patient presented no further episodes in the clinical follow-up.Comparable literature findings and therapeutic options for these abnormalities are discussed with regard to the presented case. Duodenal duplication cysts are rare congenital abnormalities which are more commonly diagnosed in infancy and childhood.However, in rare cases, these lesions can remain asymptomatic until adulthood. The combination of duplication cyst and pancreas divisum is extremely rare and both conditions have been linked with acute recurrent pancreatitis. We present the case of a 37 years-old patient who presented with repeated episodes of an acute pancreatitis. By way of magnetic resonance imaging and endoscopic ultrasonography we discovered a duplication cyst whose cavity received drainage from the dorsal pancreas. After opening the cyst cavity to the duodenal lumen with a needle knife the patient presented no further episodes in the clinical follow-up. Compara tor literature findings and therapeutic options for these abnormalities are discussed with regard to the presented case.