特发性肺含铁血黄素沉着症(Idiopathic Pulmonany Hemosiderosis,简称IPH),是一种少见病,1864年由Trichow首先发现,1931年Cee1en尸解时发现并报道,国内于1960年吴桂兰首次报道.此病主要见于小儿及年青人,病因尚不清楚,早期临床症状不典型,往往易误诊.1981年至1985年我科共收治有典型临床表现特发性肺 Idiopathic Pulmonany Hemosiderosis (IPH) is a rare disease. It was first discovered by Trichow in 1864 and was discovered and reported in 1931 when Cee1en was autopsied. It was first reported by Wu Guilan in 1960 in China. The disease is mainly seen in children and young people, the etiology is not clear, early clinical symptoms are not typical, often misdiagnosed .1981 to 1985 were treated in our department had a typical clinical idiopathic pulmonary