病史摘要梁姓,男,3岁,上海人。因脾脏进行性肿大10月余、巩膜黄染半年于1976年6月10日住院。住院前1个月起尿色深黄,尿胆原阳性,尿胆红质弱阳性,血胆红质3.25毫克％。患儿系第一胎第一产,足月顺产,出生体重2.7公斤。人工喂养,生长发育尚可。生后19天曾因肺炎、肠炎、败血症而住某院(当时腹部X线平片见肝管积气),经治疗而愈。以往无黄疸,贫血及出血史,无肝炎接触史,未到过血吸虫病、黑热病及疟疾流行区。家族史:父幼时患“鼓胀病”(有无黄疸不详),经中 Medical history Liang Surname, male, 3 years old, Shanghai. Progressive enlargement of the spleen more than 10 months, scleral yellow dye six months in June 10, 1976 hospitalization. One month before hospitalization, urine color dark yellow, urinary gallbladder positive, urine weak positive bilirubin, blood bilirubin 3.25 mg%. Pediatric first line of first birth, term full-term birth, birth weight 2.7 kg. Artificial feeding, growth and development is acceptable. 19 days after birth due to pneumonia, enteritis, sepsis and lived in a hospital (then abdominal X-ray film see the liver tube gas), the more treatment. In the past no jaundice, anemia and bleeding history, no history of hepatitis exposure, not to schistosomiasis, kala azar and malaria endemic areas. Family history: father and child suffering from “bulging disease” (with or without jaundice unknown), by