纤维肌性发育不良是一个少见疾病,该病可影响全身动脉,包括冠状动脉。该病引起的冠状动脉病变包括远端变细、长而平缓的狭窄,常可出现自发性冠状动脉夹层、血管壁内血肿、冠状动脉痉挛、冠状动脉扭曲。纤维肌性发育不良引起的冠状动脉病变可导致急性冠状动脉综合征、左心室功能不全或心源性猝死。药物治疗包括抗血小板药物、β受体阻滞药等,少数患者需经皮冠状动脉介入治疗或冠状动脉旁路术。 Fibromous dysplasia is a rare condition that affects the whole body arteries, including the coronary arteries. The disease caused by coronary lesions include distal thinning, long and flat stenosis, often with spontaneous coronary dissection, vascular wall hematoma, coronary spasm, coronary distortions. Coronary artery disease caused by fibromuscular dysplasia can lead to acute coronary syndrome, left ventricular dysfunction, or sudden cardiac death. Drug therapy, including anti-platelet drugs, β-blockers and other drugs, a small number of patients required percutaneous coronary intervention or coronary artery bypass surgery.