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目的：分析儿童郎罕细胞组织细胞增生症骨骼病变的影像学表现和特点，阐述其在本症临床诊断中作用。方法：搜集了经病理证实的儿童郎罕细胞组织细胞增生症３５例。其中男性２１例，女性１４例。年龄８个月～１０岁，平均３．７５岁。除Ｘ线平片外，１８例还进行了ＣＴ扫描，其中单纯平扫１０例，平扫加增强８例。结果：本组中颅骨破坏２１例，占６０％。脊柱５例，占１４．３％。长骨１３例，占３４．４％。扁平骨和不规则骨１５例，占４２％。勒一雪病、韩一雪一柯综合症及中间型以颅骨破坏为主，而嗜酸性肉芽肿则以长骨和脊柱为主。结论：本症的骨骼病变在Ｘ线影像学上有较特殊的表现，是临床诊断和鉴别诊断的重要手段，有时甚至可起到决定性的作用，此外还能观察疗效，了解有无复发等。
OBJECTIVE: To analyze the imaging features and features of skeletal lesions of Langerhans cell histiocytosis in children, and to elucidate its role in the clinical diagnosis of this disease. Methods: A total of 35 children with Langerhans cell histiocytosis confirmed by pathology were collected. Among them, 21 males and 14 females. Aged 8 months to 10 years, an average of 3.75 years old. In addition to plain radiographs, 18 cases were also performed CT scan, including plain scan in 10 cases, plain scan and enhanced in 8 cases. Results: Skull destruction in this group 21 cases, accounting for 60%. Spinal in 5 cases, accounting for 14.3%. Long bones in 13 cases, accounting for 34.4%. Flat bone and irregular bone in 15 cases, accounting for 42%. A snow disease, a snow-Koike syndrome and the middle type of skull destruction, while the eosinophilic granuloma long bone and spine. Conclusion: The disease of skeletal lesions in X-ray imaging has a more specific performance, is an important means of clinical diagnosis and differential diagnosis, and sometimes even play a decisive role, in addition to observe the efficacy, to understand whether the recurrence.